MULTIPLE OSTEOTOMY and INTERNAL FIXATION WITH PLATE OF PATIENT WITH CONGENITAL UNILATERAL BOWING OF THE TIBIA AND NEUROFIBROMATOSIS.
MULTIPLE OSTEOTOMY and INTERNAL FIXATION WITH PLATE OF PATIENT
WITH CONGENITAL UNILATERAL BOWING OF THE TIBIA AND
NEUROFIBROMATOSIS
A Report of an Unusual Case
P. A. W. Sanjaya*
K.A.CDewi**
*Orthopaedic and Traumatology Resident, Medical Faculty Udayana University, Sanglah
General Hospital, Denpasar Bali
** Orthopaedic and Traumatology Consultant, Medical Faculty Udayana University, Sanglah
General Hospital, Denpasar Bali
INTRODUCTION
Neurofibromatosis type 1 (NF1) is a common genetic disease with a prevalence of 1
in 3000 individuals in the general population. Genetic testing is not needed to diagnose the
condition after birth because most people with NF1 will have enough signs of the condition.
Anterolateral tibial bowing is not pathognomonic for NF1.With multiple osteotomy and plate
fixation, simultaneous correction of the tibial alignment is possible.
CASE REPORT
A 15 years old female came with angulation deformity on right leg. Her parents told
that bowed leg occur since she was born. She have history of trauma when she was 2 and 7
years old. Patient also had massage in bone setter three times each after she was fallen down.
It was observed that she had a right lower limb deformity (anterolateral bowing of the
tibia). The length discrepancy 1 cm shorter on right side. Café au lait spot was detected
clinically in the body. Radiological finding shows anterolateral bowing of tibia with
thickening cortex at the middle third of tibia.
We treat patient with multiple osteotomy and internal fixation with narrow locking
plate.
DISCUSSION
We suspected our patient with Neurofibromatosis due to presentation of café au lait spot.
During operation we did not find pseudoarthrosis. Spontaneous correction of pseudoarthrosis
might be occurred in our cases. We treatanterolateral tibia bowing treatment with multiple
osteotomy and internal fixation using plate. Stable internal fixation and proper operative
technique will lead to a cure of the alignment deformity
Keyword: Neurofibromatosis, anterior tibia bowing, multiple osteotomy, internal fixation
WITH CONGENITAL UNILATERAL BOWING OF THE TIBIA AND
NEUROFIBROMATOSIS
A Report of an Unusual Case
P. A. W. Sanjaya*
K.A.CDewi**
*Orthopaedic and Traumatology Resident, Medical Faculty Udayana University, Sanglah
General Hospital, Denpasar Bali
** Orthopaedic and Traumatology Consultant, Medical Faculty Udayana University, Sanglah
General Hospital, Denpasar Bali
INTRODUCTION
Neurofibromatosis type 1 (NF1) is a common genetic disease with a prevalence of 1
in 3000 individuals in the general population. Genetic testing is not needed to diagnose the
condition after birth because most people with NF1 will have enough signs of the condition.
Anterolateral tibial bowing is not pathognomonic for NF1.With multiple osteotomy and plate
fixation, simultaneous correction of the tibial alignment is possible.
CASE REPORT
A 15 years old female came with angulation deformity on right leg. Her parents told
that bowed leg occur since she was born. She have history of trauma when she was 2 and 7
years old. Patient also had massage in bone setter three times each after she was fallen down.
It was observed that she had a right lower limb deformity (anterolateral bowing of the
tibia). The length discrepancy 1 cm shorter on right side. Café au lait spot was detected
clinically in the body. Radiological finding shows anterolateral bowing of tibia with
thickening cortex at the middle third of tibia.
We treat patient with multiple osteotomy and internal fixation with narrow locking
plate.
DISCUSSION
We suspected our patient with Neurofibromatosis due to presentation of café au lait spot.
During operation we did not find pseudoarthrosis. Spontaneous correction of pseudoarthrosis
might be occurred in our cases. We treatanterolateral tibia bowing treatment with multiple
osteotomy and internal fixation using plate. Stable internal fixation and proper operative
technique will lead to a cure of the alignment deformity
Keyword: Neurofibromatosis, anterior tibia bowing, multiple osteotomy, internal fixation